Aldehydo-l-iduronate
Webaldehyde, any of a class of organic compounds in which a carbon atom shares a double bond with an oxygen atom, a single bond with a hydrogen atom, and a single bond with … Webaldehydo-L-iduronate L-iduronate bigg.metabolite:idour biggM:idour: L-Iduronate metacyc.compound:L-Iduronate metacycM:L-Iduronate: L-iduronate …
Aldehydo-l-iduronate
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WebMPS-II (Hunter Syndrome) This syndrome results from a deficiency of α- l-iduronate-2-sulfatase, an enzyme that hydrolyses sulfated iduronic acid residues in heparan sulfate and dermatan sulfate. Dermatan sulfate and heparan sulfate accumulate in the lysosomes of affected cells. About 370 mutations of the iduronate-2-sulfatase gene, on ... WebThe present invention relates to the production of polysaccharides containing the 1- iduronate subunit, particularly but not exclusively to heparin-type polysaccharides, and also to new...
http://amigo.geneontology.org/amigo/term/CHEBI:28481 WebDec 11, 2015 · PubMed Abstract: Hunter syndrome is a rare but devastating childhood disease caused by mutations in the IDS gene encoding iduronate-2-sulfatase, a crucial enzyme in the lysosomal degradation pathway of dermatan sulfate and heparan sulfate. These complex glycosaminoglycans have important roles in cell adhesion, growth, …
WebAccession CHEBI:33820 Name iduronate Ontology chebi_ontology Synonyms None Alternate IDs None Definition None Comment None Subset 3_STAR Related Link to all genes and gene products annotated to iduronate (excluding "regulates"). Link to all direct and indirect annotations to iduronate (excluding "regulates"). Link to all direct and … WebThe present invention provides processes for the production of polysaccharides containing the L-iduronate subunit, for example, heparin-type polysaccharides. New intermediate compounds and processes developed during the production of said polysaccharides are also presented.
WebA fourth paper on the use of 2-TST was reported in 2007 by Cateni and co-workers in the effort to prepare a natural cerebroside from Euphorbiaceae. 26 These authors took advantage of the availability of the O- and N-protected amino sugar 18 (L-ribo configuration) that was previously prepared in our laboratory by 2-TST-based homologation of the …
WebAldehydo-L-iduronate: Spectrum type: 13 C NMR Spectrum (1D, 200 MHz, D 2 O, predicted) Spectrum View. Spectra Viewer Instructions... Experimental Conditions. Solvent: D 2 O: Nucleus: 13 C: Frequency: 200 MHz: Documentation. Document Description Download File Size; Peak List (TXT) Download file: 266 Bytes: Peak Assignments (TXT) ... normandy apartments west des moinesWebl-Iduronic acid (IUPAC abbr.: IdoA) is the major uronic acid component of the glycosaminoglycans (GAGs) dermatan sulfate, and heparin. It is also present in … normandy apple tart recipeWebReactome is pathway database which provides intuitive bioinformatics tools for the visualisation, interpretation and analysis of pathway knowledge. normandy and paris france mapWebAny fungal metabolite produced during a metabolic reaction in Baker's yeast ( Saccharomyces cerevisiae ). (via D-arabinose ) Related Structures. aldehydo - D -arabinose is a Enantiomer of. aldehydo-L-arabinose. Mass : 150.12990. Formula : C5H10O5. Graph View. Tree View. how to remove stubborn contact lensWebDefinition. An iduronate that is the conjugate base of aldehydo-L-iduronic acid, obtained by deprotonation of the carboxy group; major species at pH 7.3. Stars. This entity has been manually annotated by the ChEBI Team. normandy apts kcmoWebAug 22, 2024 · Idursulfase Brand name: Elaprase Drug class: Enzymes Chemical name: α-L-iduronate sulfate sulfatase Molecular formula: C 2689 H 4057 N 699 O 792 S 14 CAS number: 50936-59-9 Medically reviewed by Drugs.com on Aug 22, 2024. Written by ASHP. Introduction Uses Dosage Warnings Interactions Stability Warning Risk of Anaphylaxis how to remove stubborn carpet stainsWebAldehyde. The p-menthane-3-carboxaldehyde auxiliary system 73 has also been used to synthesize α-amino acids and heterocycles through a sequence that features a tandem … how to remove stubborn blackheads on nose